ASYMPTOMATIC PHEOCHROMOCYTOMA ASSOCISATED WITH VON RECKLINGHAUSEN’S DISEASE (NEUROFIBROMATOSIS TYPE1): CASE REPORT AL GHAMDI, H., WAGIH , S., ASHOUR W. and DEWIK, Z. * King Abdel Aziz Hospital & Oncology center, Jeddah- Al Taif* , KSA

Document Type : Original Article

Abstract

We report a case of 50 years old male with neurofibromatosis complaining of recurrent attacks of right loin pain. Clinically , the patient was normotensive ,
his body was full of neurofibromas with cafe au lait patches (Fig. 1, 2 & 3).
Catecholamine in urine was markedly elevated. No other endocrinological
abnormality depicted. CT scan abdomen revealed presence of right adrenal mass
5.9X5.9 cm with central necrosis and haemorrage (Fig. 4 & 5). I 131 metaiodobenzylguanidine (I 131-MIBG) revealed a well defined sizable area of
intense tracer accumulation at right suprarenal gland (fig. 6 & 7). The patient
was operated upon and the histopathology proved to be benign pheochromocytoma.